Disease name

모공성 홍색비강진
 Pityriasis rubra pilaris

Prevalence

<1 / 1 000 000

Inheritance

산발성, 상염색체 우성

Age of onset

신생아기, 영아기

ICD 10 code

L44.0

MIM number

173200

Summary

Pityriasis rubra pilaris is a rare chronic papulosquamous disorder of unknown etiology characterized by small follicular papules, scaly red-orange patches, and palmoplantar hyperkeratosis, which may progress to plaques or erythroderma. Although most of the cases are sporadic and acquired, a familial form of the disease exists.